Editors
Yusuf Yazici , Gulen Hatemi , Emire Seyahi and Hasan Yazici
Behet Syndrome
2nd ed. 2020
Editors
Yusuf Yazici
School of Medicine, New York University, New York, NY, USA
Gulen Hatemi
Department of Internal Medicine, Istanbul University, Istanbul, Turkey
Emire Seyahi
Department of Rheumatology, Istanbul University, Istanbul, Turkey
Hasan Yazici
Department of Medicine, Academic Hospital, Istanbul, Turkey
ISBN 978-3-030-24130-8 e-ISBN 978-3-030-24131-5
https://doi.org/10.1007/978-3-030-24131-5
Springer Nature Switzerland AG 2020
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Professor Hulusi Behet (18811948)
In the first edition of this textbook 10 years ago, I had the following dedication:
When I first started practicing rheumatology about 10 years ago, I got calls from patients saying that they had been diagnosed with Behets and did some searching online and saw that a Dr. Yazc had done a lot of work and research on the subject. Then they found another Dr. Yazc online working in New York. They wondered if I was the Dr. Yazc they were looking for. I would tell them that the Dr. Yazc they were looking for was my father and they would say, Close enough, well come and see you. I have tried to be close enough and hope that they have been right.
The last decade has only focused my efforts in this direction and made me appreciate how all this came about even more.
This book is dedicated to my wife Angie and daughters Esra and Leyla, also granddaughters of one of my coeditors; my father and of course my mother, neither of whom I can ever repay.
Yusuf Yazc
I would like to dedicate this book to my mentors, students and patients who have inspired me with the challenges they provided, to my parents Prof Kemal Alta and Dr. Bahriye Alta for their love and encouragement, my husband Dr. brahim Hatemi for his continuous understanding and support, and my daughters Piraye and Mehve for the joy and hope they have given.
Gulen Hatemi
My history with Behet started about 20 years ago; when I met Professor Yazc and he offered me to do the prognosis survey. Thereby, I plunged in the world of Behet. Since there were no phone number in the majority of the files, I had to go to their addresses. So I chased almost all, in almost all parts of Istanbul, somewhat obsessively, went their home, been their guest, drunk their tea, talked about their health and tried to understand them. Some went blind or disabled, some had forgotten what they had in their youth, some other were dead. Since then I devoted myself to understand this amazing disease.
I would like to dedicate this book to Hasan Yazc whom I owe my profession and critical thinking, to my husband Nurhan Seyahi and my children Larissa and Aras Seyahi.
Emire Seyahi
Preface
In this second edition of our textbook on Behet syndrome, our primary aim remains the same: to be a comprehensive and compact guide to help the clinicians from various disciplines, as well as the general physician to recognize and manage Behet syndrome.
As such, the context is mainly clinical. On the other hand, our excellent contributors, presented, discussed, and referenced what is controversial and not known. We hope Behet Syndrome will also be a valuable source of ideas and a guide to the research oriented.
We would like to thank all our contributors, new and old, to both editions of this book. We would also like to thank our mentors, who have led and shaped us into who we are today, and of course our patients; at the end of the day we hope we have been able to cure some, treat most and help all, in ways small and large.
Hasan Yazici and Yusuf Yazici
Gulen Hatemi
Emire Seyahi
Yusuf Yazc
Gulen Hatemi
Emire Seyahi
Hasan Yazc
New York, NY, USA Istanbul, Turkey
Contents
Hasan Yazici
Colin G. Barnes and Yusuf Yazici
Sebahattin Yurdakul
M. Cem Mat , Dongsik Bang , Eun-So Lee and Zekayi Kutlubay
Ylmaz zyazgan and Ilknur Tugal-Tutkun
Ugur Uygunoglu and Aksel Siva
Yesim Ozguler , Sinem Nihal Esatoglu , Emire Seyahi and Melike Melikoglu
Sebahattin Yurdakul and Pietro Leccese
Jae Hee Cheon , Ibrahim Hatemi and Aykut Ferhat elik
Johannes Nowatzky and zzet Fresko
Emire Seyahi and Isabelle Kon-Paut
Cuyan Demirkesen , Bge Oz and Sha Gksel
Farida Fortune and Gulen Hatemi
Giacomo Emmi , Matteo Becatti , Alessandra Bettiol , Claudia Fiorillo and Domenico Prisco
Haner Direskeneli and Gher Saruhan-Direskeneli
Ahmet Gl and Graham R. Wallace
Idan Goldberg , Ehud Baharav , Abraham Weinberger and Ilan Krause
Emire Seyahi and David Saadoun
Gonca Mumcu , Yusuf Yazici and Gulen Hatemi
Vedat Hamuryudan , Ina Ktter and Hasan Tzn
Cetin Ezber , Eileen Radziunas , Richard West and Yusuf Yazici